EARLY DIAGNOSIS OF A RARE PULMONARY VASCULAR CONDITION: THE NEED FOR A HIGH INDEX OF SUSPICION, A GOOD NETWORK, AND THE RIGHT TOOLS
Anno:
2024
Pulmonary veno-occlusive disease (PVOD) is a rare and deadly form of pulmonary arterial hypertension (PAH), characterized by preferential venular involvement/obliteration. This leads to reduced diffusion capacity of the lung (DLCO), oxygen desaturation, and pathognomonic alterations at chest computed tomography (CT): mediastinal lymph node enlargement, centrilobular ground-glass opacities, smooth thickening…