A NEGLECTED RARE DISORDER: IGG4 RELATED DISEASE
Anno:
2024
IgG4-related disease (IgG4-RD) is an autoimmune disorder characterized by infiltration of plasma cells with IgG4. Almost any organ could be affected. Common presentations include lung manifestation, autoimmune pancreatitis, retroperitoneal fibrosis and tubulointerstitial nephritis. Cardiovascular involvement is less frequent. Corticosteroids are first line therapy, with or without anti-rheumatic drugs. Long-term…