Associazione Nazionale Medici Cardiologi Ospedalieri

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TAVI in patient suffering from Niemann – Pick disease (acid sphingomyelinase deficiency) with concomitant situs inversus and dextrocardia
Anno:
2023
Abstract Acid sphingomyelinase deficiency (ASMD) – also known as Niemann-Pick (NP) disease – is a rare, autosomal recessive disorder which is characterized by deficiency of the lysosomal enzyme acid sphingomyelinase (ASM), thus resulting in excessive storage of lipids in organs (i.e. spleen, liver, lung, bone marrow, lymph nodes, and…
Does cardiac amyloidosis ever hide a severe aortic stenosis A case report
Anno:
2023
Case presentation: A 89-year-old man, with an history of paroxysmal atrial fibrillation and chronic renal disease, was admitted to our ER for acute decompensated heart failure. He reported dyspnea on minimal exertion and worsening peripheral edema. He had a history of heart failure and a severe aortic stenosis first diagnosed in 2020…
MYOCARDIAL WORK EVALUATION IN PATIENTS WITH SEVERE AORTIC STENOSIS UNDERGOING TRANSCATHETER AORTIC VALVE REPLACEMENT
Anno:
2023
Background: il myocardial work (MW) è una tecnica ecocardiografica che permette di studiare la performance del ventricolo sinistro. Essa supera i limiti dell’ecocardiografia speckle tracking (STE) dipendenti dal post-carico, che risulta aumentato nei pazienti con stenosi aortica (AS) severa. Obiettivi: valutare gli indici di performance miocardica ottenuti con il…